|
KMID : 1144020200160010027
|
|
Journal of Korean Association for Disability and Oral Health
2020 Volume.16 No. 1 p.27 ~ p.34
|
|
|
Dental treatment in a patient with dystrophic epidermolysis bullosa under general anesthesia: A case report
|
|
Choi Won-Seok
Lee Sang-Ho
Lee Nan-Young
Kim Doo-Soo
Kim Ji-Woong
Yoon Ga-Ram
Jih Myeong-Kwan
|
|
|
Abstract
|
|
|
|
Epidermolysis Bullosa (EB) is a rare genetic disease that causes pain and results in peeling of the skin and mucous membranes, as well as easy blistering due to minor trauma or friction. EB is classified into four types according to the layer where the tissue is desquamated and blisters form. There are three genetic disorder-type EB diseases, namely, epidermolysis bullosa simplex (EBS), junctional epidermolysis bullosa (JEB), and dystrophic epidermolysis bullosa (DEB), as well as an acquired autoimmunity disorder. DEB shows autosomal recessive or dominant inheritance, and is characterized by deformities in the skin including coalescence of the fingers, blisters, scars, abnormalities of the fingertips, and milia. In extreme cases, a narrow esophagus or airway, ankyloglossia, microglossia, or squamous cell carcinoma may be seen. Dental problems associated with EB include microstomia or ankyloglossia, caused by scarring due to repeated blistering, as well as a high risk of dental caries due to difficulty in controlling a toothbrush (in turn due to hand and finger scarring). Therefore, continuous regular examination and preventive care are important. In this case report, we describe the dental treatment applied under general anesthesia for rampant caries in a 9-year-old patient with DEB who visited Chosun University Dental Hospital.
|
|
|
KEYWORD
|
|
|
Ankyloglossia, Dental treatment, Dystrophic epidermolysis bullosa, General anesthesia, Microstomia
|
|
|
FullTexts / Linksout information
|
|
|
|
|
|
Listed journal information
|
|
|
|
|